Abstract
Paroxysmal nocturnal hemoglobinuria is a rare acquired disorder of clonal hematopoietic stem cells and it is characterized as a hypercoagulable disorder. We report a 36-year-old woman with the rare triad of paroxysmal nocturnal hemoglobinuria, cerebral sinus thrombosis triggered by infection, and rapid-onset heparin-induced thrombocytopenia after resensitization of heparin. This case raises caution for heparin-induced thrombocytopenia in paroxysmal nocturnal hemoglobinuria.
MeSH terms
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Adult
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Anticoagulants / adverse effects*
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Anticoagulants / immunology
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Autoantibodies / blood
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Fatal Outcome
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Female
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Hemoglobinuria, Paroxysmal / complications*
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Hemoglobinuria, Paroxysmal / drug therapy*
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Heparin / adverse effects*
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Heparin / immunology
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Humans
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Meningitis, Aseptic / complications
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Sinus Thrombosis, Intracranial / diagnostic imaging
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Sinus Thrombosis, Intracranial / drug therapy
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Sinus Thrombosis, Intracranial / etiology*
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Thrombocytopenia / chemically induced*
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Thrombocytopenia / diagnosis
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Thrombocytopenia / immunology
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Tomography, X-Ray Computed
Substances
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Anticoagulants
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Autoantibodies
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Heparin